Anti-AK5 antibody autoimmune encephalitis

Evidence-based neurology checklist on anti-ak5 antibody autoimmune encephalitis: Pathogenesis This is caused by anti-adenylate kinase 5 antibody This is a nucleoside monophosphate kinase Pathological features Neurological features Psychiatric features Absent features Cerebrospinal fluid (CSF)…

Pathogenesis

  • This is caused by anti-adenylate kinase 5 antibody
  • This is a nucleoside monophosphate kinase

Pathological features

Neurological features

Psychiatric features

Absent features

Cerebrospinal fluid (CSF) analysis

Magnetic resonance imaging (MRI) brain

Outcome

References

  1. Do LD, Chanson E, Desestret V, et al. Characteristics in limbic encephalitis with anti-adenylate kinase 5 autoantibodies. Neurology 2017; 88:514-524. 
  2. Ng AS, Kramer J, Centurion A, et al. Clinico-pathological correlation in adenylate kinase 5 autoimmune limbic encephalitis. J Neuroimmunol 2015; 287:31-35.
  3. Vicino A, Loser V, Salvioni Chiabotti P, Brouland JP, Du Pasquier R. Anti-adenylate kinase 5 encephalitis with histologic evidence of CNS vasculitis. Neurol Neuroimmunol Neuroinflamm 2021; 8:e1010.
  4. McKeon-Makki I, McKeon A, Yang B, et al. Adenylate kinase 5 (AK5) autoimmune encephalitis: clinical presentations and outcomes in three new patients. J Neuroimmunol 2022; 367:577861.
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