Tuberous sclerosis complex (TSC): monitoring

Evidence-based neurology checklist on tuberous sclerosis complex (tsc): monitoring: Baseline assessments 3-generation family history Blood pressure assessment for hypertension Respiratory function: dyspnoea, cough Renal function Skin examination Neuropsychiatric symptoms: for TAND Clinical…

Baseline assessments

  • 3-generation family history
  • Blood pressure assessment for hypertension
  • Respiratory function: dyspnoea, cough
  • Renal function
  • Skin examination
  • Neuropsychiatric symptoms: for TAND

Clinical monitoring

TAND monitoring

Magnetic resonance imaging (MRI) brain monitoring

Electroencephalogram (EEG) monitoring

Magnetic resonance imaging (MRI) abdomen monitoring

Cardiac monitoring

Lymphangioleiomyomatosis (LAM) monitoring

Acronym

References

  1. Northrup H, Aronow ME, Bebin EM, et al. Updated International Tuberous Sclerosis Complex diagnostic criteria and surveillance and management recommendations. Pediatr Neurol 2021; 123:50-66.
  2. Northrup H, Krueger DA; International Tuberous Sclerosis Complex Consensus Group. Tuberous sclerosis complex diagnostic criteria update: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol 2013; 49:243-254.
  3. Curatolo P, Moavero R, de Vries PJ. Neurological and neuropsychiatric aspects of tuberous sclerosis complex. Lancet Neurol 2015; 14:733-745.
  4. Amin S, Kingswood JC, Bolton PF, et al. The UK guidelines for management and surveillance of Tuberous Sclerosis Complex. QJM 2019; 112:171-182.
  5. And 0 more. Subscribe to see the full list

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