Neuromuscular respiratory dysfunction: investigations

Evidence-based neurology checklist on neuromuscular respiratory dysfunction: investigations: Respiratory evaluation Vital capacity (VC) Cough peak flow Arterial blood gases Spirometry and volumes Maximal muscle pressures Peak cough expiratory flow Sniff nasal inspiratory force (SNIF Test)…

Respiratory evaluation

  • Vital capacity (VC)
  • Cough peak flow
  • Arterial blood gases
  • Spirometry and volumes
  • Maximal muscle pressures
  • Peak cough expiratory flow
  • Sniff nasal inspiratory force (SNIF Test)
  • Trans-diaphragmatic pressure
  • Phrenic nerve stimulation
  • Ultrasound scan evaluation of diaphragm
  • Respiratory pattern

Oropharyngeal evaluation

Annual assessment of sleep-disordered breathing: indications

References

  1. Hull J, Aniapravan R, Chan E, et al. British Thoracic Society guideline for respiratory management of children with neuromuscular weakness. Thorax 2012; 67:i1-i40.
  2. Shahrizaila N, Kinnear WJM, Wills AJ. Respiratory involvement in inherited primary muscle conditions. JNNP 2006; 77:1108-1115.
  3. Mehta S. Neuromuscular disease causing acute respiratory failure. Respir Care 2006; 51:1016-1021.
  4. Gilchrist JM. Overview of neuromuscular disorders affecting respiratory function. Semin Respir Crit Care Med 2002; 23:191-200.
  5. Farrero E, Antón A, Egea CJ, et al. Guidelines for the management of respiratory complications in patients with neuromuscular disease. Arch Bronconeumol 2013; 49:306-313.
  6. And 1 more. Subscribe to see the full list

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