Explore / PRION DISEASES PRION DISEASES neurology checklists Explore evidence-based neurology topics and fully referenced clinical checklists covering PRION DISEASES. Creutzfeldt Jakob disease (CJD)Creutzfeldt Jakob disease (CJD): clinical featuresCreutzfeldt Jakob disease (CJD): differential diagnosisCreutzfeldt Jakob disease (CJD): investigationsCreutzfeldt Jakob disease (CJD): treatmentNew variant Creutzfeldt Jakob disease (nvCJD)Familial prion diseasesFamilial Creutzfeldt Jakob disease (fCJD)Gerstmann Sträussler Scheinker (GSS) syndromeFatal familial insomnia (FFI): clinical featuresFatal familial insomnia (FFI): investigationsSporadic fatal insomnia (SFI)Sporadic fatal insomnia (SFI): clinical featuresSporadic fatal insomnia (SFI): pathologySporadic fatal insomnia (SFI): investigationsOther prion diseasesKuruVariably protease-sensitive prionopathy (VPSPr)